141 top medical experts on Refsum Disease across 13 countries and 4 U.S. states, including 12 MDs (Physicians). This is based on an objective analysis of their Scientific Publications, Clinical Trials, Medicare, and NIH Grants.
- Refsum Disease: An autosomal recessive familial disorder that usually presents in childhood with polyneuropathy; sensorineural hearing loss; ichthyosis; ataxia; retinitis pigmentosa; and cardiomyopathies. (From Joynt, Clinical Neurology, 1991, Ch37, p58-9; Rev Med Interne 1996;17(5):391-8) This condition can be caused by mutation in the genes encoding peroxisomal phytanoyl-CoA hydroxylase or proteins associated peroxisomal membrane, leading to impaired catabolism of phytanic acid in peroxisomes.
- Clinical guidelines are the recommended starting point to understand initial steps and current protocols in any disease or procedure:
- Broader Categories (#Experts): Hereditary Sensory and Motor Neuropathy (1,703), Inborn Metabolic Brain Diseases (1,358), Peroxisomal Disorders (437).
- Clinical Trials : at least 7 including 1 Completed, 4 Recruiting
- Synonyms: HMSN Type IV, Heredopathia Atactica Polyneuritiformis, Type IV Hereditary Motor and Sensory Neuropathy, Phytanic Acid Storage Disease
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