202 top medical experts on Inclusion Body Myopathy With Early-Onset Paget Disease And Frontotemporal Dementia across 12 countries and 13 U.S. states, including 35 MDs (Physicians). This is based on an objective analysis of their Scientific Publications, Clinical Trials, Medicare, and NIH Grants.

  1. Inclusion Body Myopathy With Early-Onset Paget Disease And Frontotemporal Dementia: Inclusion body myopathy with Paget disease of bone and frontotemporal dementia (IBMPFD) is a multisystem degenerative genetic disorder characterized by adult-onset proximal and distal muscle weakness (clinically resembling limb-girdle muscular dystrophy; see this term); early-onset Paget disease of bone (see this term), manifesting with bone pain, deformity and enlargement of the long-bones; and premature frontotemporal dementia (see this term), manifesting first with dysnomia, dyscalculia and comprehension deficits followed by progressive aphasia, alexia, and agraphia. As the disease progresses, muscle weakness begins to affect the other limbs and respiratory muscles, ultimately resulting in respiratory or cardiac failure.
  2. Clinical guidelines are the recommended starting point to understand initial steps and current protocols in any disease or procedure:
  3. Support Organizations
  4. Synonyms: IBMPFD,  Inclusion Body Myopathy with Early-Onset Paget Disease of Bone and-or Frontotemporal Dementia,  Inclusion Body Myopathy with Paget Disease of Bone and-or Frontotemporal Dementia,  Lower Motor Neuron Degeneration With Paget-Like Bone Disease,  With Paget Disease Of Bone Limb-Girdle Muscular Dystrophy,  Pagetoid Amyotrophic Lateral Sclerosis,  Pagetoid Neuroskeletal Syndrome


  

        

                    


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