70 top medical experts on Aagenaes syndrome across 6 countries and 1 U.S. states, including 3 MDs (Physicians). This is based on an objective analysis of their Scientific Publications, Clinical Trials, Medicare, and NIH Grants.
- Aagenaes syndrome: Cholestasis-lymphedema syndrome is a rare genetic disorder characterized by neonatal intrahepatic cholestasis, often lessening and becoming intermittent with age, and severe chronic lymphedema which mainly affects the lower limbs. Patients often present with fat malabsorption leading to failure to thrive, fat soluble vitamin deficiency with bleeding, rickets, and neuropathy. In 25% of cases, cirrhosis occurs during childhood or later in life.
- Clinical guidelines are the recommended starting point to understand initial steps and current protocols in any disease or procedure:
- Support Organizations
- Encephalitis Society
32 Castlegate
Malton, North Yorkshire YO17 7DT
United Kingdom
Telephone: +44 (0)1653 699599
E-mail: support@encephalitis.info
Website: http://www.encephalitis.info/
Social media: Twitter: @encephalitis Facebook: /encephalitissociety
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- Synonyms: Cholestasis lymphedema syndrome, Cholestasis-Lymphedema Syndrome, Lymphedema - cholestasis syndrome, Lymphedema-Cholestasis Syndrome
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