26 top medical experts on 1 congenital Bile acid synthesis defect across 4 countries, including 3 MDs (Physicians). This is based on an objective analysis of their Scientific Publications, Clinical Trials, Medicare, and NIH Grants.
- 1 congenital Bile acid synthesis defect: Congenital bile acid synthesis defect type 1 (BAS defect type 1) is the most common anomaly of bile acid synthesis (see this term) characterized by variable manifestations of progressive cholestatic liver disease, and fat malabsorption.
- Clinical guidelines are the recommended starting point to understand initial steps and current protocols in any disease or procedure:
- Synonyms: Deficiency Of 3-Beta-Hydroxy-Delta-5-C27-Steroid Oxidoreductase, 3-beta-hydroxy-delta-5-C27-steroid oxidoreductase deficiency, progressive familial intrahepatic 4 Cholestasis, Congenital Bile Acid Synthesis Defect Type 1 (CBAS1), PFIC4 Progressive familial intrahepatic cholestasis type 4, Progressive familial intrahepatic cholestasis 4
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